Double Uterus-hemivagina-renal Agenesis Syndrome


Double uterus, hemivagina and renal agenesis is a rare congenital urogenital anomaly characterized by the presence of double uterus (didelphys, bicornuate or septum-complete or partial), unilateral cervico-vaginal obstruction (obstructed hemivagina-communicant, not communicant or septate and unilateral cervical atresia) and ipsilateral renal anomalies (renal agenesis (see this term) and/or other urinary tract anomalies). Patients are usually diagnosed at puberty after menarche due to recurrent severe dysmenorrhea, chronic pelvic pain, excessive foul smelling mucopurulent discharge, spotting and intermenstrual bleeding (depending on the existence of uterine or vaginal communications). Fever, dyspareunia, and a palpable abdominal, pelvic or vaginal mass (mucocolpos or pyocolpos) may also be present.

Clinical Features

Top most frequent phenotypes and symptoms related to Double Uterus-hemivagina-renal Agenesis Syndrome

  • Fever
  • Premature birth
  • Renal agenesis
  • Breech presentation
  • Chronic pain
  • Uterus didelphys
  • Dysmenorrhea
  • Dyspareunia
  • Metrorrhagia
  • Hydrocolpos

And another 3 symptoms. If you need more information about this disease we can help you.

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Incidence and onset information

— Currently we don't have prevalence information about this disease (Not enough data available about incidence and published cases.)
No data available about the known clinical features onset.

Alternative names

Double Uterus-hemivagina-renal Agenesis Syndrome Is also known as obstructed hemivagina and ipsilateral renal anomaly, ohvira syndrome, herlyn-werner syndrome, double uterus and obstructed hemivagina syndrome, wunderlich syndrome.

Researches and researchers

Currently, we don't have any information about doctors, researches or researchers related to this disease. Please contact us if you would like to appear here.

Sources and references

You can check the following sources for additional information.

ORPHANET MESH OMIM Rare Disease Search Engine

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