1. Mendelian
  2. Rare Diseases
  3. TEMPORAL ARTERITIS

Juvenile Temporal Arteritis

Table of contents:

Description

Juvenile temporal arteritis (JTA) is an extremely uncommon vasculitis of unknown etiology. Eleven documented cases have been reported in the literature, affecting older children and young adults. In contrast to the classic form of temporal arteritis, it is not a systemic disease nor does it cause local symptoms at the temporal area. The term JTA was coined by Lie and his colleagues, in 1975, when they reported four cases of an otherwise asymptomatic disease presenting with a painless nodule at the temporal region. None of the cases showed evidence of systemic disease or history of trauma to the temporal region. Excisional biopsy of the lesions revealed a non-giant cell granulomatous inflammation of the temporal arteries with eosinophilic infiltration, intimal proliferation and microaneurysmal disruption of the media. JTA has a benign clinical course, is treated by surgical excision and does not recur.

Clinical Features

Phenotypes and symptoms related to Juvenile Temporal Arteritis

  • Headache
  • Vasculitis
  • Conjunctivitis
  • Eosinophilia
  • Leukocytosis
  • Cerebral ischemia
  • Skin nodule
  • Allergic rhinitis
  • Arteritis

Incidence and onset information

— Currently we don't have prevalence information about this disease (Not enough data available about incidence and published cases.)
— No data available about the known clinical features onset.

Alternative names

Juvenile Temporal Arteritis Is also known as jta, non-giant cell granulomatous temporal arteritis with eosinophilia.

Researches and researchers

Doctors, researchs, and experts related to Juvenile Temporal Arteritis extracted from public data.

Juvenile Temporal Arteritis Experts map



Current Researchs and researchers

  • BERLIN — Pr Henning ZEIDLER

    Coordinator of research network

    • Institution/s:
      — Geschäftsstelle Kompetenznetz-Rheuma
    • Research area/topic::

      Competence Network Rheumatic Diseases


  • CAMBRIDGE — Dr David JAYNE

    Coordinator of expert centre - Principal investigator of clinical trial - Investigator of clinical trial - Coordinator of research network

    • Institution/s:
      — Cambridge University Hospitals NHS Foundation Trust, Addenbrooke's Hospital
    • Research area/topic::

      EUVAS: European vasculitis study group


Sources and references

You can check the following sources for additional information.

ORPHANET Rare Disease Search Engine

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